Article

GSTF Journal of Advances in Medical Research (JAMR)

, 1:4

First online:

Open Access This content is freely available online to anyone, anywhere at any time.

A Functional Univentricle: Large Ventricular Septal Defect, Atrioventricular Discordance, Malposition of the Great Arteries, Pulmonary Stenosis, and Major Aorto Pulmonary Collaterals

  • Cristine Catindig-SantelicesAffiliated withSection of Cardiology, University of the Philippines- Philippine General Hospital (UP-PGH)
  • , Michael Joseph T. ReyesAffiliated withSection of Cardiology, University of the Philippines- Philippine General Hospital (UP-PGH)
  • , Melgar MatulacAffiliated withSection of Cardiology, University of the Philippines- Philippine General Hospital (UP-PGH)
  • , Maycibel Macadaeg-CaperoAffiliated withSection of Pedriatric Cardiology, University of the Philippines- Philippine General Hospital (UP-PGH)
  • , Frederick P. GloriaAffiliated withSection of Cardiology, University of the Philippines- Philippine General Hospital (UP-PGH)

Abstract

We report a case of a 25 year-old male with a functionally univentricular heart. He underwent consult for clearance prior to employment and has been asymptomatic since childhood with good functional capacity, his 6 minute walk test was normal at 300 meters. Pertinent physical findings were a right ventricular heave, a grade 3/6 systolic murmur over the 2nd-3rd intercostal spaces left parasternal border, a continuous murmur over the interscapular area and cyanosis of the nailbeds. Laboratory exams showed mild erythrocytosis and hypoxemia. Transthoracic and transesophageal echocardiographic findings showed a large ventricular septal defect (apical intraventricular septum remnant), atrioventricular discordance, malposition of the great arteries and severe pulmonary stenosis. Major aorto-pulmonary collaterals were demonstrated on hemodynamics study. Patient is stable and living a normal life but advised to avoid moderate to heavy strenuous activities. He is on a regular follow – up at our out patient clinic and there are no planned immediate surgical interventions at present.

Keywords

Univentricular Heart Large Ventricular Septal Defect Pulmonic Stenosis Malposition of the Great Arteries Major Aorto Pulmonary Collaterals